Title:

Zwyrodnienie wątrobowo- soczewkowe z przewagą uszkodzeń korowo-podkorowych

Subtitle:

HEPATOLENTICULAR DEGENERATION WITH PREDOMINANCE OF CORTICO-SUBCORTICAL LESIONS

Creator:

Mossakowski, Mirosław Jan (1929 - 2001) ; Kasperek, Stefan ; Rościszewska, Danuta

Publisher:

Państwowy Zakład Wydawnictw Lekarskich

Place of publishing:

Warszawa

Date issued/created:

1964

Subject and Keywords:

hepatolenticular degeneration ; cortico-bubcortical lesions

Abstract:

Two cases of Wilson’s disease are reported, in which cortico-subcortical lesions of the frontal lobes predominated, with only slight changes in the basal gangliaThe clinical picture of the condition in the 17-year-old female and 21-year-olc male patient was characterized by the presence of the pyramidal syndrome, epileptic seizures and mental changes superimposed on the typical Wilson type of extrapyramidal syndrome. Biochemical studies confirmed the diagnosis oi hepatolenticular degeneration. The Keiser-Fleischer ring was not found in the male patient.

Relation:

Neuropatologia Polska

Volume:

2

Issue:

2

Start page:

145

End page:

165

Resource Type:

Article

Format:

pdf

Language:

pol

Language of abstract:

eng ; rus

Rights:

Creative Commons Attribution BY 4.0 license

Terms of use:

Copyright-protected material. [CC BY 4.0] May be used within the scope specified in Creative Commons Attribution BY 4.0 license, full text available at: ; -

Digitizing institution:

Mossakowski Medical Research Center PAS

Original in:

Library of the Mossakowski Medical Research Center PAS

Projects co-financed by:

Operational Program Digital Poland, 2014-2020, Measure 2.3: Digital accessibility and usefulness of public sector information; funds from the European Regional Development Fund and national co-financing from the state budget.