<?xml version="1.0" encoding="UTF-8"?>
<?xml-stylesheet type="text/xsl" href="https://www.rcin.org.pl/style/common/xsl/oai-style.xsl"?>
<OAI-PMH xmlns="http://www.openarchives.org/OAI/2.0/" 
         xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance"
         xsi:schemaLocation="http://www.openarchives.org/OAI/2.0/
         http://www.openarchives.org/OAI/2.0/OAI-PMH.xsd">
	<responseDate>2026-06-12T01:10:45Z</responseDate>
	<request identifier="oai:rcin.org.pl:133963" metadataPrefix="oai_dc" verb="GetRecord">
	https://rcin.org.pl/oai-pmh-repository.xml</request>
	<GetRecord>
	
  <record>
	<header>
		<identifier>oai:rcin.org.pl:133963</identifier>
	    <datestamp>2022-02-01T15:50:11Z</datestamp>
		  <setSpec>rcin.org.pl</setSpec> 	      <setSpec>rcin.org.pl:partnerCollections:imdik:failes</setSpec> 	      <setSpec>rcin.org.pl:scientificDataAndObjects:medicalScience</setSpec> 	      <setSpec>rcin.org.pl:partnerCollections:imdik</setSpec> 	      <setSpec>rcin.org.pl:partnerCollections:imdik:failes:neuro</setSpec> 	      <setSpec>rcin.org.pl:scientificDataAndObjects</setSpec> 	      <setSpec>rcin.org.pl:scientificDataAndObjects:medicalScience:fileOfMedicalCases</setSpec> 	      <setSpec>rcin.org.pl:partnerCollections</setSpec> 	    </header>
		<metadata>
	<oai_dc:dc xmlns:dc="http://purl.org/dc/elements/1.1/" xmlns:oai_dc="http://www.openarchives.org/OAI/2.0/oai_dc/" xmlns:xsi="http://www.w3.org/2001/XMLSchema-instance" xsi:schemaLocation="http://www.openarchives.org/OAI/2.0/oai_dc/ http://www.openarchives.org/OAI/2.0/oai_dc.xsd">
<dc:title xml:lang="en"><![CDATA[Files for neuromuscular diseases (2006) nr 34/06]]></dc:title>
<dc:title xml:lang="pl"><![CDATA[Kartoteka przypadków klinicznych chorób nerwowo-mięśniowych (2006) - opis nr 34/06]]></dc:title>
<dc:creator><![CDATA[Fidziańska-Dolot, Anna (1930–2015)]]></dc:creator>
<dc:subject xml:lang="en"><![CDATA[Cogenital myopathy]]></dc:subject>
<dc:subject xml:lang="pl"><![CDATA[Miopatia wrodzona]]></dc:subject>
<dc:description xml:lang="en"><![CDATA[Muscle segment examination in light and electron microscopy]]></dc:description>
<dc:description xml:lang="en"><![CDATA[A 13-year-old patient with suspected congenital myopathy was examined. A biopsy quadriceps sinister was performed. Electronmicroscopy analysis revealed most of the muscle fibers of the correct diameter (Fig.1). In such fibers , centrally located myocyte nuclei present (Fig.2,3,4). In some myocytes disorganization of the myofibrils of the contractile apparatus observed (fig.5,6,7,8,9,10,11). The mitochondria in the ultrastructurally altrered myocytes were damaged, characterized by light mitochondrial matrix and lack of mitochondrial cristae (Figes 12,13,14).]]></dc:description>
<dc:description xml:lang="pl"><![CDATA[Badanie wycinka mięśniowego w mikroskopie świetlnym i elektronowym]]></dc:description>
<dc:description xml:lang="pl"><![CDATA[Fig.1. Włókna mięśniowe o prawidłowej średnicy. Fig.2,3,4. Jądra miocytó położone centralnie. Fig.5,6,7,8,9,10,11, Dezorganizacja miofibryli w obrębie aparatu kurczliwego. Fig.12,13,14. Uszkodzone mitochondria z widocznymi ubytkamu grzebieni.]]></dc:description>
<dc:contributor><![CDATA[Mossakowski Medical Research Center Polish Academy of Sciences. Department of Neuromuscular]]></dc:contributor>
<dc:contributor><![CDATA[Instytut Medycyny Doświadczalnej i Klinicznej PAN. Zakład Badawczo-Leczniczy Chorób Nerwowo-Mięśniowych]]></dc:contributor>
<dc:date><![CDATA[2006]]></dc:date>
<dc:type xml:lang="en"><![CDATA[Text]]></dc:type>
<dc:type xml:lang="en"><![CDATA[Image]]></dc:type>
<dc:type xml:lang="pl"><![CDATA[Tekst]]></dc:type>
<dc:type xml:lang="pl"><![CDATA[Obraz]]></dc:type>
<dc:format xml:lang="en"><![CDATA[pdf]]></dc:format>
<dc:format xml:lang="pl"><![CDATA[pdf]]></dc:format>
<dc:identifier><![CDATA[https://rcin.org.pl/dlibra/publication/168571/edition/133963/content]]></dc:identifier>
<dc:identifier><![CDATA[oai:rcin.org.pl:133963]]></dc:identifier>
<dc:language><![CDATA[pol]]></dc:language>
<dc:relation><![CDATA[oai:rcin.org.pl:publication:168571]]></dc:relation>
<dc:rights xml:lang="en"><![CDATA[Creative Commons Attribution BY 4.0 license]]></dc:rights>
<dc:rights xml:lang="pl"><![CDATA[Licencja Creative Commons Uznanie autorstwa 4.0]]></dc:rights>
</oai_dc:dc>

</metadata>
	  </record>	</GetRecord>
</OAI-PMH>
